A rare cause of irrevocable childhood alopecia feigning alopecia universalis: Atrichia congenita with papular lesions

Atrichia congenita with papular lesions is rare, autosomal recessive condition that leads to complete hairloss which irreversible and keratin filled lesions. An insertion mutation in the exon 2 of hairless gene responsible for hairloss. Middle lower portions hair follicle are replaced by keratinizing cysts absence shafts. We here reporting a case 8-year-old girl over scalp, eyebrows, eyelashes, body started at birth was gradual 9 months age on view its rarity misdiagnosis.